226,011 research outputs found
Genetic heterogeneity in Cornelia de Lange syndrome (CdLS) and CdLS-like phenotypes with observed and predicted levels of mosaicism
No full textCornelia de Lange syndrome (CdLS) is a multisystem disorder with distinctive facial appearance, intellectual disability and growth failure as prominent features. Most individuals with typical CdLS have de novo heterozygous loss-of-function mutations in NIPBL with mosaic individuals representing a significant proportion. Mutations in other cohesin components, SMC1A, SMC3, HDAC8 and RAD21 cause less typical CdLS
Lange and Hayek Revisited: Lessons from Czech Voucher Privatization
No full textA fundamental question in economics since the 1930s has been whether an administrative price system could simulate the results of perfect competition even without a true market for the means of production. The theoretical possibility of such a system has been known since the introduction of market socialism by Oskar Lange. We have used the artificial bidding market involved in the Czech voucher privatization process to test whether a sequential process of trial-and-error can set administrative prices close to equilibrium. It would appear from this natural experiment that Robbins and Hayek were correct in doubting the real-world feasibility of market socialism.Bidding scheme, Oskar Lange’s model, Privatization, Price setting, Voucher scheme
Lange and Hayek Revisited: Lessons from Czech Voucher Privatization
No full textA fundamental question in economics since the 1930s has been whether an administrative price system could simulate the results of perfect competition even without a true market for the means of production. The theoretical possibility of such a system has been known since the introduction of market socialism by Oskar Lange. We have used the artificial bidding market involved in the Czech voucher privatization process to test whether a sequential process of trial-and-error can set administrative prices close to equilibrium. It would appear from this natural experiment that Robbins and Hayek were correct in doubting the real-world feasibility of market socialism.bidding scheme; Oskar Lange’s model; privatization; price setting; voucher scheme
Dr Willem De Lange - Update Report for Mediation
No full text1 The Te Puru Group, involving 5 properties at the southern end of the Te Puru fan-delta, agreed to engage in ‘without prejudice’ discussions with Council.
2 I have previously prepared evidence for the Te Puru Group relating to the nature of the coastal hazards affecting their properties and the location of the CEL. A key finding was that the Te Puru fan-delta (an alluvial fan that is prograding into a water body) is an accretionary landform that is continuing to accrete, primarily in response to episodic events (debris flows). In my opinion, accretion is likely to continue in the future.
3 The Te Puru Group have provided me with a letter to the TCDC, dated 15 September 2016 and marked Without Predjudice, which is attached as Appendix A. I have read this letter, which outlines a number of suggestions to allow specified activities seaward of the CEL by affected landowners.
4 Subsequent to the hearing, additional data have become available on the evolution of the fan-deltas of the Western Coromandel, including Te Puru. This document summarises the additional data and discusses the implications for the potential shoreline changes at the southern end of Te Puru fan-delta pertinent to the suggestions made in the letter
The dynamics of visual representations under top-down modulation
No full textContains fulltext :
200655.pdf (Publisher’s version ) (Open Access)Radboud University, 24 januari 2019Promotor : Lange, F.P. de Co-promotor : Kok, P.164 p
Dispelling the Myths Behind First-author Citation Counts
No full textWe conducted a full-scale evaluative citation analysis study of scholars in the XML research field to explore just how different from each other author rankings resulting from different citation counting methods actually are, and to demonstrate the capability of emerging data and tools on the Web in supporting more realistic citation counting methods. Our results contest some common arguments for the continued
use of first-author citation counts in the evaluation of scholars, such as high correlations between author rankings by first-author citation counts and other citation
counting methods, and high costs of using more realistic citation counting methods that are not well-supported by the ISI databases. It is argued that increasingly available digital full text research papers make it possible for citation analysis studies to go beyond what the ISI databases have directly supported and to employ more
sophisticated methods
Femme - Souillure. Citation de Frédéric Lange : Manger ou les jeux et les creux du Plat, éd. du Seuil
No full textLange Frédéric. Femme - Souillure. Citation de Frédéric Lange : Manger ou les jeux et les creux du Plat, éd. du Seuil. In: Sorcières : les femmes vivent, n°1, 1975. La nourriture. p. 40
Femme - Souillure. Citation de Frédéric Lange : Manger ou les jeux et les creux du Plat, éd. du Seuil
No full textLange Frédéric. Femme - Souillure. Citation de Frédéric Lange : Manger ou les jeux et les creux du Plat, éd. du Seuil. In: Sorcières : les femmes vivent, n°1, 1975. La nourriture. p. 40
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