2,472 research outputs found
Attraversando la pittura di Caravaggio. Novità e scoperte sui procedimenti e sulla tecnica del ciclo Contarelli
No full textThymosin beta arg10, a major variant of thymosin beta 10 in rabbit tissues.
No full textTwo homologous peptides, designated thymosin beta 4 and thymosin beta 10, respectively, have been shown to be widely distributed in mammalian cells and tissues (S. Erickson-Viitanen, S. Ruggieri, P. Natalini, and B.L. Horecker (1983) Arch. Biochem. Biophys. 221, 570-576; S. Erickson-Viitanen, S. Ruggieri, P. Natalini, and B.L. Horecker, (1983) Arch. Biochem. Biophys. 225, 407-413). In the rabbit, thymosin beta 4 is replaced by a variant, thymosin beta ala4, that contains alanine in place of serine at the blocked NH2-terminus. It is reported that in rabbit tissues thymosin beta 10 is also replaced by a variant, designated thymosin beta arg10, that contains an additional amino acid, arginine, inserted following lysine-38. The rabbit tissues analyzed also differ from those of other mammals in the relative quantities of thymosin beta ala4 and beta arg10, which are nearly equal, compared to tissues from other mammals where the quantities of thymosin beta 10 are only one-third to one-tenth those of thymosin beta 4
Spectrum of skeletal abnormalities in a complex malformation syndrome with "cutis tricolor" (Ruggieri-Happle syndrome)
No full textBackground: The term cutis tricolor describes the combination of congenital hyper- and hypopigmented skin lesions in close proximity to each other in a background of normal complexion. This phenomenon has been reported: (i) as a purely cutaneous trait; (ii) as a part of a complex malformation syndrome (Ruggieri-Happle syndrome - RHS); (iii) as a distinct type [cutis tricolor parvimaculata]; (iv) in association with other (e.g. vascular) skin disturbances. Objectives: To delineate the spectrum of skeletal defects in cutis tricolor. Methods: Retrospective and prospective analysis of skeletal surveys in 14 subjects (eight men; six women; aged 2-28 years) with cutis tricolor [4 purely cutaneous trait; 10 syndromic (RHS)]. Results: Bone abnormalities were recorded in 71.4% (10/14) of patients [100% (10/10) of cases with (other-than-skeletal) extra-cutaneous manifestations vs. null (0/4) in cases with purely cutaneous traits] and included overall small skull (n = 6); prognathism (n = 6); 'J'-shaped pituitary fossa (n = 1); absence of atlas posterior arch (n = 3); frontal bossing (n = 6); scoliosis (n = 9) with kyphosis (n = 6) and/or lordosis (n = 6); vertebral (n = 9) and ribs (n = 4) defects. Negative ZFHX1B gene analyses excluded overlaps with Mowat-Wilson syndrome. Conclusions: Cutis tricolor may be a marker of underlying skeletal involvement particularly in subjects with a complex syndromic (RHS) phenotype. © 2010 The Author(s)/Acta Pædiatrica © 2010 Foundation Acta Pædiatrica
Complex malformation (Ruggieri-Happle) phenotype with "cutis tricolor" in a 10-year-old girl
No full textThe term cut is tricolor describes the combination of congenital hyper- and hypo-pigmented skin lesions in close proximity to each other in a background of normal complexion. It is currently regarded as a twin-spotting phenomenon and today is clear that not all cases of cutis tricolor represent one single entity. This phenomenon has been reported so far: (a) as an isolated skin manifestation; (b) as a part of a complex malformation syndrome (Ruggieri-Happle syndrome - RHS); (c) as a distinct phenotype [cut is tricolor parvimaculata]; (d) in association with other (e.g., vascular) skin disturbances. We report a novel case of cutis tricolor in a 10-year-old girl who had dysmorphic facial features [alike those seen in cases with syndromic (RHS) cutis tricolor], overall overgrowth [weight, length, and head circumference were >90th percentile; there was increased bone age], mild cognitive delay (current IQ = 55), behavioural disturbances, febrile seizures and (later) partial complex epilepsy (currently under good control), and skeletal defects [i.e., posterior scalloping of the lumbar vertebrae]. We discuss the main similarities and differences between the various phenotypes in the spectrum of cutis tricolor and with other conditions sharing features with the present case. (C) 2012 The Japanese Society of Child Neurology. Published by Elsevier B.V. All rights reserved
Moving to higher ground: Planning for relocation as an adaptation strategy to climate change in the Fiji Islands
No full textThis edited volume advances our understanding of climate relocation (or planned retreat), an emerging topic in the fields of climate adaptation and hazard risk, and provides a platform for alternative voices and views on the subject.
As the effects of climate change become more severe and widespread, there is a growing conversation about when, where and how people will move. Climate relocation is a controversial adaptation strategy, yet the process can also offer opportunity and hope. This collection grapples with the environmental and social justice dimensions from multiple perspectives, with cases drawn from Africa, Asia, Australia, Oceania, South America, and North America. The contributions throughout present unique perspectives, including community organizations, adaptation practitioners, geographers, lawyers, and landscape architects, reflecting on the potential harms and opportunities of climate-induced relocation. Works of art, photos, and quotes from flood survivors are also included, placed between sections to remind the reader of the human element in the adaptation debate. Blending art – photography, poetry, sculpture – with practical reflections and scholarly analyses, this volume provides new insights on a debate that touches us all: how we will live in the future and where?
Challenging readers’ pre-conceptions about planned retreat by juxtaposing different disciplines, lenses and media, this book will be of great interest to students and scholars of climate change, environmental migration and displacement, and environmental justice and equity
La libreria mediceo-laurenziana, architettura di Michelagnolo Buonarroti
No full textopera misurata, disegnata, e intagliata da Ferdinando Ruggieri architettoTomo 4, parte 1: Piante ed alzati interiori ed esterni dell'insigne chiesa di S. Maria del Fiore metropolitana fiorentinaTomo 4, parte 2: La libreria mediceo-laurenziana, architettura di Michelagnolo BuonarrotiHandschriftliches Exlibris: "Luchini B.(?) i 3 tomi comprati da C. Ruggieri. 1745." 990006294620205503_0001 Exemplar der ETH-BI
Callistocythere Ruggieri 1953
No full textGenus CALLISTOCYTHERE Ruggieri, 1953 114. C. hayamensis Hanai, 1957 a Aladin, 1987: 820; Gvozdeva et al., 1997: 27; Schornikov & Sokolenko, 1999 a: 181; 1999 b: 216; Schornikov & Zenina, 2004 b: 215, figs. 2 (9, 10). 115. C. ishizakii Ikeya & Zhou, 1992 Schornikov & Chavtur, 2001: 92; 2002: 95; Schornikov & Zenina, 2004 b: 215. 116. C. subjaponica Hanai, 1957 a Aladin, 1987: 820 (C. sp.); Schornikov & Chavtur, 2001: 92; 2002: 95; Schornikov & Zenina, 2004 b: 215. 117. C. sp. 3 Schornikov & Chavtur, 2001: 92; 2002: 95; Schornikov & Zenina, 2004 b: 215.Published as part of Schornikov, Evgeny I., 2006, Checklist of the ostracod (Crustacea) fauna of Peter the Great Bay, Sea of Japan, pp. 29-59 in Zootaxa 1294 on page 42, DOI: 10.5281/zenodo.17351
Turismo, piccole isole e cambiamenti climatici: le politiche della Repubblica di Fiji tra mitigazione e adattamento
No full textNella regione del Pacifico meridionale, riconosciuta quale “climate-tourism hotspot”, la Repubblica di Fiji rappresenta una tra le principali mete turistiche, con flussi e investimenti in costante aumento. L’estremizzazione climatica, tuttavia, ha messo in luce la vulnerabilità del comparto turistico del paese rendendo necessaria l’adozione di strategie atte a incrementarne la resilienza. Il piano di politiche climatiche 2018-2030 di Fiji individua nel settore turistico – in particolare nell’eco-turismo - un player fondamentale sia per lo sviluppo economico, sia per il potenziamento della tutela ambientale. Senza trascurare il contributo del turismo ai cambiamenti climatici, questo diventa anche un importante alleato nell’implementazione di azioni di mitigazione e adattamento di un piccolo stato insulare in via di sviluppo, con ricadute sull’intera società. L’obiettivo del presente contributo è quello di analizzare le modalità attraverso cui il turismo è individuato e, conseguentemente, impiegato quale settore chiave nella costruzione della resilienza climatica di Fiji alla luce del ruolo di leadership climatica assunto su scala regionale e globale.Nella regione del Pacifico meridionale, riconosciuta quale «climate-tourism hotspot», la Repubblica di Fiji
rappresenta una tra le principali mete turistiche, con flussi e investimenti in costante aumento. L’estremizzazione
climatica, tuttavia, ha messo in luce la vulnerabilità del comparto turistico del Paese rendendo necessaria l’adozione di
strategie atte a incrementarne la resilienza. Il piano di politiche climatiche 2018-2030 di Fiji individua nel settore
turistico – in particolare nell’eco-turismo – un player fondamentale sia per lo sviluppo economico sia per il potenziamento
della tutela ambientale. Senza trascurare il contributo del turismo ai cambiamenti climatici, questo diventa anche un
importante alleato nell’implementazione di azioni di mitigazione e adattamento di un piccolo stato insulare in via di
sviluppo, con ricadute sull’intera popolazione. L’obiettivo del presente contributo è quello di analizzare le modalità
attraverso cui il turismo è individuato e, conseguentemente, impiegato quale settore chiave nella costruzione della resilienza
climatica di Fiji alla luce del suo ruolo di leadership climatica su scala regionale e globale
Profili Professionali dei corsi di Laurea di area pedagogica: le rappresentazioni sociali degli studenti
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