43 research outputs found
Platelet Satellitism: A Unique Cause of Pseudothrombocytopenia
No full textLetter showing a unique report of platelet satellitis
Children with lysinuric protein intolerance: Experience from a lower middle income country
No full textBACKGROUND: Lysinuric protein intolerance (LPI) is an inborn error of metabolism consequential to recessive mutations in the SLC7A7 gene. The metabolic imbalance in absorption and excretion of dibasic amino acids is considered the basis of LPI. The disease results from protein intolerance with signs and symptoms oscillating from cerebral impairment, respiratory involvement, renal failure and autoimmune complications. AIM: To determine biochemical and clinical presentation of cases with biochemical picture suggestive of LPI in Pakistani children. METHODS: The study was conducted at the Biochemical Genetic Lab, Department of Pathology and Laboratory Medicine, AKU Plasma, and urine amino acid quantification data from January 2013 to October 2018 was included in this study. The amino acids were analyzed by high performance liquid chromatography. Prestructured requisition forms were used to obtain the clinicopathological data. Statistical analysis was done by Microsoft Excel 2017. RESULTS: A total of 6 patients were recognized. All the patients were male (100%). The mean age was 24 mo ± 10 d. All the patients had low plasma concentration of lysine, ornithine and arginine, whereas increased levels of lysine, ornithine and arginine in urine were observed in 2 patients. History of consanguineous marriage was present in all patients (100%). The most observed clinical symptom was feeding difficulty followed by failure to thrive (83.3%) and developmental delay (66.6%). Hepatomegaly was present in all patients (100%). No mutation analysis was done. CONCLUSION: This study portrays the biochemical and clinical spectrum of LPI in Pakistan. Although clinical manifestations appeared in the first 2 years of life, most of them suffered a delay in undergoing diagnostic workup
Proceedings of ASEAN - Pakistan Conference on Materials Science
No full textDr. Arnir Hussain
Important Factors for high Performance of Composites
Dr Bilal Khan, Dr. Zaffar Khan
Polymer Nanocomposites: Prospects, Potentials and Applications in Aerospace Structures
M Arshad Bashir, Noaman-ul-Haq, Shamshad Ahmed, M Bilal Khan
Synthesis and Mechanical Properties Evaluations of Ablative Materials
Priyo Sardjono, Bambang Prihandoko
Ceramic Graphite Composite as Anode of Lithium Battery
M. Anis-ur-Rehman, S. Nasir, A. Maqsood
Structural, Electrical and Magnetic Studies of Co-precipitated Ni-Co Nano-Ferrites
M Babar Saeed, M Fahim Hashmi
Control Of Thermoplastic Polyimide Properties Through Molecular Architecture
A. Haider, M Shoaib, M Asim, M Farooque
Comparative Investigation of Barium Titanate Ceramics Synthesized by Conventional
Powder and Sol-gel Techniques
Dr. Zaffar. M Khan
The On-Line Condition Monitoring System of Composite Structures Using Fiber Optic Sensors
Muhammad Faisal, Muhammad Shahid
Corrosion behavior of "ASTM A-106 Grade-A carbon steel in amine solutions
under sour conditions.
Mohammad Fuzail, Sabir Ghafoor Alvi, Shamshad Ahmed, Jamil Anwar
Study of the influence of DOP Mobilizer on the Mechanical and Thermal Properties
of the Irradiated Semi-Crystalline Ethylene-Propylene Copolymer
Syed Jawid Askari, Abid Hameed, Usama Umer, Ah Imran Merchant, Noman Danish
The Role of Nucleation Density and Methane Fraction in the Growth of Diamonds
Coatings and Titanium: A Review
Muhammad Mazhar Iqbal, Sajid Raza Ch
Design Optimization and Material Selection for Liquid Propellant Tanks
K Maaz, A. Mashiatullah, R M Qureshi, S. Karim, G. Ali, T. Javed
Morphological studies of NixCol-xFe2O4 ( 1) Magnetic Nanoparticles
M H. Saleh, E.A. Othman, F. Ismail, M Mohammad
Characterization of Nanocrystalline Neodymium Iron Boron (NdFeB) Magnetic Materials.
Nguyen Nang Dinft, Le Ha Chi, Tran Thi Chung Thuy, Hyung-Kook Kim
Characterization of multilayer organic light diodes using nanostructured composite thin films
Amir Habib, Nils stelzer, Roland haubner
Solvothermal synthesis of tetragonal BaTiO3
R.J. Talib, A.H Hashim, M A. Hamid, M R.M Toff , J. J. Mohamed
Mechanical and tribological properties of plasma carbonitrided stainless steel aisi 316
M. Bilal Khan, Saleem Hussain
Enhancement of Mechanical Properties of Kevlar-Epoxy Composite by Improving
the Interface Coupling
Sultan Mahmood, M Bilal Khan, Toqeer Kausar, Faiz -ur- Rehman
Hot Drawing & Characterization of Ultra High Molecular Weight Polyethylene
(UHMWPE) Fibers to Produce High Impact Resistant & Light Weight Armor Composites
Zainul Huda
Recent Developments In Thermal Barrier Coatings (Tbc) On Turbine Blades
And Their Inspection Techniques
Syed J. Ali, Chaudhary J. Omer, Nasir M Ahmad, Christopher J. Barrett, Muhammad I. Sarwar
Novel Functionalized Polymers Containing Photoresponsive Azobenzene
Chromophore: Synthesis and Characterization
A.Quddos, S.M.Hussain, A.Wadood, A.Hayat
Syntheses, Charcterization And Incorporation Of Nanoparticles Into The Polymer Matrix
A.S. Khan, F.S.L.Wong, LU.Rehrnan
Synthesis and in-vitro analysis of a novel bioactive nano-composite
Noaman Ul-Haq, Joong Kon Park, M Bilal Khan, Khairuddin Sanaullah
Chiral Resolution of Phenylalanine using Ultrafiltration Technique by Molecularly
Imprinted Membrane
M. Bilal Khan
Intelligent Viscoelastic Polyurethane Intrinsic Nano Composites
Shamshad Ahmed, M Junaid Afzal, Mazhar Mehmood
Role of Compatibilizers in Improvement of Mechanical and Thermal Properties of EPDM and Polypropylene Blends
Christian Lammel
Induction aided manufacturing of nano-filled polymers and CRF
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Technological impact on the art of moviemaking: deploying new and convergent media to redefine a model for Pakistan’s cinema
No full textThis thesis examines the decline in Pakistani cinema during the last two decades. It examines the history of the cinema and exposes some possible, previously ignored, causes for that decline. This research led the author to ask “Can new and convergent media be helpful in reviving the Pakistani cinema?” The thesis introduces the ideas of established and emergent cinema, building on the work of Williams (1977) in discussing the ideas of dominant, residual and emergent culture. The exploration reveals two gaps in the film industry: first, the lack of training in the making of films; and, second, the change in possible production methods allowed by new and emergent technologies. The thesis addresses both of these gaps by suggesting new production paradigms which incorporate the new technology and by examining two scripts to develop methodologies for teaching. The scripts are produced into films as the practice section of the research. The first film, creative element 1, is developed using some of the new tehnologies, students as crew and the available resources of an educational establishment to test the methodologies that have been derived. The outcomes of the creative element 1 laid the foundation of the second film, creative element 2. It is shot on mobile phones and distributed from Pakistan through Vimeo with a negligible budget. The social networks helped to arrange equipment and locations and allowed extreme freedom to the filmmaker
