102,210 research outputs found
Progetto di recupero e valorizzazione dell’area nodale Arco del Sacramento nel centro storico di Benevento
No full textIl volume pubblica le relazioni di progetto e gli elaborati grafici dei gruppi che hanno partecipato al Concorso per il recupero e la valorizzazione dell'Area Nodale dell'Arco del Sacramento, bandito dall'Amministrazione Comunale di Benevento.
Il testo presenta la proposta del gruppo coordinato da Marco Cenacchi.
Il progetto è stato segnalato dalla Giuria
Emerging new entities and variants of tumors of CNS neoplasms
No full textAbstract. Since the appearance in 2000 of the World Health Organization (WHO) classification for central nervous system (CNS) neoplasms, numerous descriptions of new entities or variants have appeared in the literature. In the group of neuronal and mixed glioneuronal neoplasms are lesions with distinctive morphological features that are still not included in a precise classification, including extraventricular neurocytoma, papillary glioneuronal tumor, rosette-forming glioneuronal of the fourth ventricle, glioneuronal with neuropil-like rosette, and DNT-like tumor of the septum pellucidum. The glioneuronal tumor with neuropil-like rosette and oligodendroglioma with neurocytic differentiation represent morphological variants of genetically proven diffuse gliomas. The lipoastrocytoma and the pilomixoid astrocytoma enlarge the group of astrocytic lesions. Rare, low-grade gliomas of the spinal cord with extensive leptomeningeal dissemination associated with unusual neuroimaging are described. The chordoid glioma of the third ventricle and the papillary tumor of the pineal region seem to be correlated by a common histogenesis from the specialized ependyma of the subcommissural organ. An embryonal tumor with neuropil and true rosettes combining features of neuroblastoma and ependymoblastoma is discussed. These new, recently described lesions indicate that the complex morphologic spectrum of CNS tumors is far from being completely delineated
1995-2002: la riqualificazione del quartiere Barco a Ferrara. Evoluzione di un programma complesso
No full textL'articolo presenta, in una prospettiva cronologica, le diverse fasi della riqualificazione del Barco, quartiere di abitazioni popolari nella città di Ferrara, realizzato negli anni ’40 per ospitare i lavoratori occupati nelle industrie chimiche, oggetto dal 1995 di un intervento di riqualificazione attuato dallo IACP e da ACER
The clinical and molecular spectrum of autosomal dominant limb-girdle muscular dystrophies focusing on ransportinopathy.
No full textIntroduction: Limb-girdle muscular dystrophies (LGMD) are a clinical and genetically heterogeneous
group of muscle diseases presenting with a phenotypic spectrum. Autosomal dominant LGMDs represent
less than 10% of the group and are subdivided, according to the last classification, in five dominant
LGMD forms (type D1-D5), in which mutations in various genes have been identified. Dominant LGMD
might be due to a defect of DNAJB6 (LGMD D1), transportin-3 (LGMD D2, TNPO3-related), mutations in
HNRNPDL gene (LGMD D3), in CAPN3 gene (LGMD D4) and in collagen 6 (LGMD D5, collagen 6-related).
Areas covered: We present the pathomechanism of dominant LGMDs and clinical management of
respiratory and bulbar complications. We analyze the clinical presentation of cases affected by LGMD
D2 in a large Italo-Spanish family. We consider two main phenotypic entities: the childhood form
developing the clinical features in the first decade of life and the late-onset phenotype, that present
distinct clinical, histopathological and MRI features. The main features in dominant LGMDs, such as
LGMD D1, D3, D4, D5 are highlighted, including the differential ones with other dystrophies.
Expert opinion: Early diagnosis of LGMD, utilizing Next Generation Sequencing technique (NGS), is
crucial for offering an accurate diagnosis. Muscle MRI imaging is emerging both for diagnosis and
follow-up of disease progression
Muscle Pathology in Biopsy of MuSK-Ab Positive Myasthenic Patients Shows Mitochondrial Abnormalities
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[Chordoid tumor of the 3d ventricle: immunohistochemical and ultrastructural study of 3 cases].
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Malignant Large Cell Calcifying Sertoli Cell Tumor of the Testis (LCCSCTT). Report of a case in an elderly man and review of the literature
No full textDevelopment of a computational tool for limiter edge plasma modeling with application to IGNITOR
No full textIGNITOR is the only experiment today designed with the ambitious goal of achieving ignition. During the discharge, the First-Wall Limiter (FWL) will receive about 20 MW [B. Coppi, A. Airoldi, F. Bombarda, et al., Nucl. Fusion 41 (2001) 1253-1257] power, split between conduction/convection and radiation channels. Previous estimates suggested a peak heat flux on the FWL close to 1 MW/m2. This value should be re-evaluated, accounting for the latest developments in the design of the IGNITOR first wall and changes in the operational scenarios, in order to assess the risk of damages to the FWL deriving from the combination of thermal and mechanical stresses. For this purpose, the development of the ASPOEL code, implementing a 2D model of the edge plasma and including a detailed representation of the FWL, was started at Politecnico di Torino. Here we present the main features of the new code, and illustrate its potential via a preliminary application to IGNITO
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